What foods should not be eaten by people with phenylketonuria

What foods can't be eaten by people with phenylketonuria? Most people don't know much about phenylketonuria, so they don't know what to pay attention to in their diet. But if you don't pay attention to your diet, the disease will relapse even if you are cured. So, let's learn about what foods can't be eaten by people with phenylketonuria!

Phenylketonuria is a genetic metabolic disease caused by reduced activity of phenylalanine hydroxylase in the body or deficiency of its coenzyme tetrahydrobiopterin, which leads to obstruction of phenylalanine metabolism to tyrosine, increased phenylalanine concentration in the blood and tissues, and significant increase of phenylpyruvate, phenylacetate and phenyllactic acid in the urine, hence the name "phenylketonuria".

1. Children with phenylketonuria have special requirements for protein in their diet

Since phenylalanine is mostly found in protein, children with phenylketonuria have very special requirements for protein. Their requirements for other nutrients: sugar, fat, vitamins, and minerals (including trace elements) are the same as those of normal children.

2. A low-phenylalanine diet is recommended

It is not enough to eat ordinary food alone. They must eat some special phenylalanine-free (or low) protein. This protein is artificially made and belongs to a special type of nutritional food specially developed. Secondly, children with phenylketonuria must also consume enough protein, otherwise it will affect their growth and development.

3. Special nutritional foods

In order to grow and develop, 80% of the protein they need every day must be supplied by artificial special nutritional foods, such as:

1) Phenylalanine-free (or low) nutritional powder-----commonly known as milk powder:

2) Phenylalanine-free (or low) protein powder:

It is not a terrible thing for children with phenylketonuria to adopt a low-phenylalanine diet. As long as parents have the patience to make a delicious, fragrant and tasty diet for their children, the children can grow up happily and healthily, become excellent students, and become useful talents for the country in the future. However, during this treatment process, parents need to maintain a certain degree of patience and accompany their children to grow up healthily.

3) Low-phenylalanine staple foods for phenylketonuria - for example: staple flour, noodle flour, dumpling flour, self-raising flour, starch rice, etc. Because rice and noodles are also "high" phenylalanine foods for children with phenylketonuria.

2. What other foods can children with phenylketonuria eat besides the above special foods?

There are many foods that can be eaten, such as:

1. Starchy foods

Vermicelli, rice noodles, jelly, lotus root, lotus root powder, water chestnut, potato, yam, sweet potato, cassava, taro, pumpkin, etc.:

2. Sugar

White sugar, glucose, fructose, lactose, maltose, etc.:

3. Fats

Various vegetable oils (peanut oil, soybean oil, rapeseed oil, sunflower oil, sesame oil, olive oil, coconut oil, medium-chain fatty acids (MCT), etc.).

4. Animals that have had their oil residue removed after refining

Pig, beef, mutton, chicken, duck, goose fat, butter, margarine, etc.:

5. Low-phenylalanine foods

Fruits and vegetables (Note: beans among vegetables, such as beans, cowpeas, soybeans, mung beans, kidney beans, etc. cannot be eaten).